Medullary Cystic Kidney Disease

Autosomal dominant tubulointerstitial kidney disease progressing to ESRD.

What it is

A genetic disorder that forms cysts in the medulla, causes salt wasting, and leads to gradual kidney failure.

Prevalence

Rare; accounts for 10–25% of pediatric end-stage renal disease cases.

Symptoms to watch

Easy bruising, fatigue, itching, muscle twitching, gout, excessive urination, salt craving, weight loss, seizures.

Treatment options

Hydration and salt supplements, medication and diet changes to slow decline, dialysis, and transplant for advanced disease.

Medullary Cystic Kidney Disease

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